Queston #27421Note

Sturge-Weber syndrome is a neurocutaneous genetic disorder with angiomas involving the leptomeninges, choroid, and face, also known as a “port-wine stain”. Patients typically present with refractory epilepsy with multiple seizure types and contralateral hemiplegia. This MRI T1 sequence with contrast showcases prominent leptomeningeal enhancement and dilation of transparenchymal veins. Gyriform calcifications can be appreciated on CT scans and are described as the “tram-track sign