Von Hippel-Lindau (VHL) – presents with numerous benign and malignant tumors in various organs 
– CNS hemangioblastomas occur in 60-80% of VHL patients 
– Cerebellar hemagioblastomas can present with headache, ataxia, and increased intracranial pressure 

 

Findings on pathology consistent with hemangioblastoma include: 

1. numerous thin-walled vessels lined with abundant vascular cells